This is a 55 year old female who has sustained 2 pneumothoracies and had bilateral pleurodesis. Otherwise she is mildly short of breath. PFT’s show an FEV1 of 69% predicted an FEV1/FVC ratio of .50. Her DlCO is 79% of predicted. She has not smoked and the alpha-1 level is normal
Please offer a differential diagnosis






Posted by rochesterlunggroup